Neurofibromatosis type 1 (NF1) is an autosomal dominant condition affecting approximately 1 in 3000 live births. The manifestations of this condition are extremely variable, even within families, and genetic counseling is consequently difficult with regard to prognosis. Individuals with NF1 are acknowledged to be at increased risk of malignancy. Several studies have previously attempted to quantify this risk, but have involved relatively small study populations. Soft tissue tumors represent a heterogeneous group of mesenchymal and neural lesions. We report a case of giant scalp Fibrosarcoma of the scalp in patient with neurofibromatosis type I without intracranial extension, in a 35 year old female which was excised completely along with the involved overlying skin, and reconstruction was done to cover the defect using trapezius flap and split thickness skin graft from the right thigh. She is doing well after treatment and is in regular follow up while awaiting further management by the oncologists.
Published in | International Journal of Neurologic Physical Therapy (Volume 3, Issue 5) |
DOI | 10.11648/j.ijnpt.20170305.12 |
Page(s) | 44-48 |
Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
Copyright |
Copyright © The Author(s), 2017. Published by Science Publishing Group |
Neurofibromatosis Type I, Fibrosarcoma, Trapezius Flap, Scalp Defect
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APA Style
Kantenga Dieu Merci Kabulo, Patrice Ntenga, Kelvin Nemayire, Nathanael Harunangoni Zimani, Aaron Musara, et al. (2017). Trapezius Flap Reconstruction of Scalp Defect After Removal of Occipital Fibrosarcoma in Neurofibromatosis Type I Patient. International Journal of Neurologic Physical Therapy, 3(5), 44-48. https://doi.org/10.11648/j.ijnpt.20170305.12
ACS Style
Kantenga Dieu Merci Kabulo; Patrice Ntenga; Kelvin Nemayire; Nathanael Harunangoni Zimani; Aaron Musara, et al. Trapezius Flap Reconstruction of Scalp Defect After Removal of Occipital Fibrosarcoma in Neurofibromatosis Type I Patient. Int. J. Neurol. Phys. Ther. 2017, 3(5), 44-48. doi: 10.11648/j.ijnpt.20170305.12
AMA Style
Kantenga Dieu Merci Kabulo, Patrice Ntenga, Kelvin Nemayire, Nathanael Harunangoni Zimani, Aaron Musara, et al. Trapezius Flap Reconstruction of Scalp Defect After Removal of Occipital Fibrosarcoma in Neurofibromatosis Type I Patient. Int J Neurol Phys Ther. 2017;3(5):44-48. doi: 10.11648/j.ijnpt.20170305.12
@article{10.11648/j.ijnpt.20170305.12, author = {Kantenga Dieu Merci Kabulo and Patrice Ntenga and Kelvin Nemayire and Nathanael Harunangoni Zimani and Aaron Musara and Sitshengiso Matshalaga and Kusezweni Kevin Nduku and Rudo Makunike-Mutasa and Kazadi Kaluile Ntenga Kalangu}, title = {Trapezius Flap Reconstruction of Scalp Defect After Removal of Occipital Fibrosarcoma in Neurofibromatosis Type I Patient}, journal = {International Journal of Neurologic Physical Therapy}, volume = {3}, number = {5}, pages = {44-48}, doi = {10.11648/j.ijnpt.20170305.12}, url = {https://doi.org/10.11648/j.ijnpt.20170305.12}, eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ijnpt.20170305.12}, abstract = {Neurofibromatosis type 1 (NF1) is an autosomal dominant condition affecting approximately 1 in 3000 live births. The manifestations of this condition are extremely variable, even within families, and genetic counseling is consequently difficult with regard to prognosis. Individuals with NF1 are acknowledged to be at increased risk of malignancy. Several studies have previously attempted to quantify this risk, but have involved relatively small study populations. Soft tissue tumors represent a heterogeneous group of mesenchymal and neural lesions. We report a case of giant scalp Fibrosarcoma of the scalp in patient with neurofibromatosis type I without intracranial extension, in a 35 year old female which was excised completely along with the involved overlying skin, and reconstruction was done to cover the defect using trapezius flap and split thickness skin graft from the right thigh. She is doing well after treatment and is in regular follow up while awaiting further management by the oncologists.}, year = {2017} }
TY - JOUR T1 - Trapezius Flap Reconstruction of Scalp Defect After Removal of Occipital Fibrosarcoma in Neurofibromatosis Type I Patient AU - Kantenga Dieu Merci Kabulo AU - Patrice Ntenga AU - Kelvin Nemayire AU - Nathanael Harunangoni Zimani AU - Aaron Musara AU - Sitshengiso Matshalaga AU - Kusezweni Kevin Nduku AU - Rudo Makunike-Mutasa AU - Kazadi Kaluile Ntenga Kalangu Y1 - 2017/10/28 PY - 2017 N1 - https://doi.org/10.11648/j.ijnpt.20170305.12 DO - 10.11648/j.ijnpt.20170305.12 T2 - International Journal of Neurologic Physical Therapy JF - International Journal of Neurologic Physical Therapy JO - International Journal of Neurologic Physical Therapy SP - 44 EP - 48 PB - Science Publishing Group SN - 2575-1778 UR - https://doi.org/10.11648/j.ijnpt.20170305.12 AB - Neurofibromatosis type 1 (NF1) is an autosomal dominant condition affecting approximately 1 in 3000 live births. The manifestations of this condition are extremely variable, even within families, and genetic counseling is consequently difficult with regard to prognosis. Individuals with NF1 are acknowledged to be at increased risk of malignancy. Several studies have previously attempted to quantify this risk, but have involved relatively small study populations. Soft tissue tumors represent a heterogeneous group of mesenchymal and neural lesions. We report a case of giant scalp Fibrosarcoma of the scalp in patient with neurofibromatosis type I without intracranial extension, in a 35 year old female which was excised completely along with the involved overlying skin, and reconstruction was done to cover the defect using trapezius flap and split thickness skin graft from the right thigh. She is doing well after treatment and is in regular follow up while awaiting further management by the oncologists. VL - 3 IS - 5 ER -