Ebstein anomaly is a rare congenital disease of the tricuspid valve (<1%) diagnosed at all ages. A single case of an 85 y old patient was reported in 1979 as the longest survival with ebstein anomaly who had no cardiac symptoms until 79 years old. The aim of this case report is to highlight the need for an early echocardiographic diagnosis of this disease to prevent sudden death from arrhythmias or other complications because as we see patients with ebstein anomaly can live a healthy long life asymptomatic. The patient described in this case is a 60 years old male diabetic and heavy smoker, who presented to the cardiology department with fatigue and atypical angina with dyspnea on moderate effort. Cardiac ultrasound was in favor of an isolated Ebstein anomaly type A, with partial atrialization of the right ventricle (RV) with an adequate volume of the right ventricle (17cm2) and no specific other associated anomalies. Symptoms described by the patient were purely pulmonary due to a mild obstructive disease. Patient was diagnosed with chronic obstructive lung disease due to his smoking habits. Reaching this age and being asymptomatic with conserved RV and LV function is a sign of good outcome. This case was an interesting lucky finding. It was astonishing to see a patient surviving this anomaly at 60 years old asymptomatically.
| Published in | Cardiology and Cardiovascular Research (Volume 2, Issue 3) |
| DOI | 10.11648/j.ccr.20180203.14 |
| Page(s) | 65-67 |
| Creative Commons |
This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
| Copyright |
Copyright © The Author(s), 2018. Published by Science Publishing Group |
Ebstein Anomaly, Asymptomatic, Atrialization
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APA Style
Randa Tabbah, Raffy Karaminissian. (2018). Ebstein Anomaly in a 60 Years Patient: A Lucky Finding. Cardiology and Cardiovascular Research, 2(3), 65-67. https://doi.org/10.11648/j.ccr.20180203.14
ACS Style
Randa Tabbah; Raffy Karaminissian. Ebstein Anomaly in a 60 Years Patient: A Lucky Finding. Cardiol. Cardiovasc. Res. 2018, 2(3), 65-67. doi: 10.11648/j.ccr.20180203.14
AMA Style
Randa Tabbah, Raffy Karaminissian. Ebstein Anomaly in a 60 Years Patient: A Lucky Finding. Cardiol Cardiovasc Res. 2018;2(3):65-67. doi: 10.11648/j.ccr.20180203.14
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Download@article{10.11648/j.ccr.20180203.14,
author = {Randa Tabbah and Raffy Karaminissian},
title = {Ebstein Anomaly in a 60 Years Patient: A Lucky Finding},
journal = {Cardiology and Cardiovascular Research},
volume = {2},
number = {3},
pages = {65-67},
doi = {10.11648/j.ccr.20180203.14},
url = {https://doi.org/10.11648/j.ccr.20180203.14},
eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ccr.20180203.14},
abstract = {Ebstein anomaly is a rare congenital disease of the tricuspid valve (2) and no specific other associated anomalies. Symptoms described by the patient were purely pulmonary due to a mild obstructive disease. Patient was diagnosed with chronic obstructive lung disease due to his smoking habits. Reaching this age and being asymptomatic with conserved RV and LV function is a sign of good outcome. This case was an interesting lucky finding. It was astonishing to see a patient surviving this anomaly at 60 years old asymptomatically.},
year = {2018}
}
TY - JOUR T1 - Ebstein Anomaly in a 60 Years Patient: A Lucky Finding AU - Randa Tabbah AU - Raffy Karaminissian Y1 - 2018/10/30 PY - 2018 N1 - https://doi.org/10.11648/j.ccr.20180203.14 DO - 10.11648/j.ccr.20180203.14 T2 - Cardiology and Cardiovascular Research JF - Cardiology and Cardiovascular Research JO - Cardiology and Cardiovascular Research SP - 65 EP - 67 PB - Science Publishing Group SN - 2578-8914 UR - https://doi.org/10.11648/j.ccr.20180203.14 AB - Ebstein anomaly is a rare congenital disease of the tricuspid valve (2) and no specific other associated anomalies. Symptoms described by the patient were purely pulmonary due to a mild obstructive disease. Patient was diagnosed with chronic obstructive lung disease due to his smoking habits. Reaching this age and being asymptomatic with conserved RV and LV function is a sign of good outcome. This case was an interesting lucky finding. It was astonishing to see a patient surviving this anomaly at 60 years old asymptomatically. VL - 2 IS - 3 ER -
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