A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature

Chenjun Zhang; Jiahong Xu

doi:doi:10.11648/j.ccr.20220603.11

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A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature

Chenjun Zhang, Jiahong Xu

Published in Cardiology and Cardiovascular Research (Volume 6, Issue 3)

Received: 16 April 2022 Accepted: 27 September 2022 Published: 11 October 2022

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Abstract

Left ventricular non-compaction cardiomyopathy (LVNC) has anatomic characters of prominent left ventricular trabeculation and deep recesses and relatively thiner compacted layer which can lead to structurally and functionally abnormal of heart muscle. Its pathogenesis predominantly be primary cardiomyopathy and also can be results of drug toxicity or response to acquired triggers. Our case is a 27 years old man who had appeared symptoms including dyspnea and palpitation caused by exertion about ten years and been found with atrial septal defect but had not performed intervention. Then he was admitted because of aggravation of symptoms and been diagnosed left ventricular non compaction after finished echocardiography. Afterwards because of symptomatic bradycardia he had pacemaker implantation, but three months later he died of decompensated acute heart failure. LVNC has variable clinical manifestations including heart failure, thromboembolic events, ventricular arrhythmias and heart failure and the diagnosis of LVNC depends on echocardiography and Cardiac magnetic resonance mainly. Its mortality and morbidity are high and its classification as a specific cardiomyopathy be more appropriate. Therapy of end stage myocardial failure dependes on heart transplantation. Implanted cardioverter defibrillator (ICD) or cardiac resynchronization therapy defibrillator (CRTD) is the key method to prevent from sudden death. Risk stratification includes heart failure therapy, oral anticoagulation, heart transplantation and implantation of an automated defibrillator/cardioverter.

Published in	Cardiology and Cardiovascular Research (Volume 6, Issue 3)
DOI	10.11648/j.ccr.20220603.11
Page(s)	81-85
Creative Commons	This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited.
Copyright	Copyright © The Author(s), 2022. Published by Science Publishing Group

Keywords

Left Ventricular Non-compaction, Arrhythmia, Myocardial Trabeculation

References

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APA Style

Chenjun Zhang, Jiahong Xu. (2022). A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature. Cardiology and Cardiovascular Research, 6(3), 81-85. https://doi.org/10.11648/j.ccr.20220603.11

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ACS Style

Chenjun Zhang; Jiahong Xu. A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature. Cardiol. Cardiovasc. Res. 2022, 6(3), 81-85. doi: 10.11648/j.ccr.20220603.11

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AMA Style

Chenjun Zhang, Jiahong Xu. A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature. Cardiol Cardiovasc Res. 2022;6(3):81-85. doi: 10.11648/j.ccr.20220603.11

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@article{10.11648/j.ccr.20220603.11,
  author = {Chenjun Zhang and Jiahong Xu},
  title = {A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature},
  journal = {Cardiology and Cardiovascular Research},
  volume = {6},
  number = {3},
  pages = {81-85},
  doi = {10.11648/j.ccr.20220603.11},
  url = {https://doi.org/10.11648/j.ccr.20220603.11},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ccr.20220603.11},
  abstract = {Left ventricular non-compaction cardiomyopathy (LVNC) has anatomic characters of prominent left ventricular trabeculation and deep recesses and relatively thiner compacted layer which can lead to structurally and functionally abnormal of heart muscle. Its pathogenesis predominantly be primary cardiomyopathy and also can be results of drug toxicity or response to acquired triggers. Our case is a 27 years old man who had appeared symptoms including dyspnea and palpitation caused by exertion about ten years and been found with atrial septal defect but had not performed intervention. Then he was admitted because of aggravation of symptoms and been diagnosed left ventricular non compaction after finished echocardiography. Afterwards because of symptomatic bradycardia he had pacemaker implantation, but three months later he died of decompensated acute heart failure. LVNC has variable clinical manifestations including heart failure, thromboembolic events, ventricular arrhythmias and heart failure and the diagnosis of LVNC depends on echocardiography and Cardiac magnetic resonance mainly. Its mortality and morbidity are high and its classification as a specific cardiomyopathy be more appropriate. Therapy of end stage myocardial failure dependes on heart transplantation. Implanted cardioverter defibrillator (ICD) or cardiac resynchronization therapy defibrillator (CRTD) is the key method to prevent from sudden death. Risk stratification includes heart failure therapy, oral anticoagulation, heart transplantation and implantation of an automated defibrillator/cardioverter.},
 year = {2022}
}

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TY  - JOUR
T1  - A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature
AU  - Chenjun Zhang
AU  - Jiahong Xu
Y1  - 2022/10/11
PY  - 2022
N1  - https://doi.org/10.11648/j.ccr.20220603.11
DO  - 10.11648/j.ccr.20220603.11
T2  - Cardiology and Cardiovascular Research
JF  - Cardiology and Cardiovascular Research
JO  - Cardiology and Cardiovascular Research
SP  - 81
EP  - 85
PB  - Science Publishing Group
SN  - 2578-8914
UR  - https://doi.org/10.11648/j.ccr.20220603.11
AB  - Left ventricular non-compaction cardiomyopathy (LVNC) has anatomic characters of prominent left ventricular trabeculation and deep recesses and relatively thiner compacted layer which can lead to structurally and functionally abnormal of heart muscle. Its pathogenesis predominantly be primary cardiomyopathy and also can be results of drug toxicity or response to acquired triggers. Our case is a 27 years old man who had appeared symptoms including dyspnea and palpitation caused by exertion about ten years and been found with atrial septal defect but had not performed intervention. Then he was admitted because of aggravation of symptoms and been diagnosed left ventricular non compaction after finished echocardiography. Afterwards because of symptomatic bradycardia he had pacemaker implantation, but three months later he died of decompensated acute heart failure. LVNC has variable clinical manifestations including heart failure, thromboembolic events, ventricular arrhythmias and heart failure and the diagnosis of LVNC depends on echocardiography and Cardiac magnetic resonance mainly. Its mortality and morbidity are high and its classification as a specific cardiomyopathy be more appropriate. Therapy of end stage myocardial failure dependes on heart transplantation. Implanted cardioverter defibrillator (ICD) or cardiac resynchronization therapy defibrillator (CRTD) is the key method to prevent from sudden death. Risk stratification includes heart failure therapy, oral anticoagulation, heart transplantation and implantation of an automated defibrillator/cardioverter.
VL  - 6
IS  - 3
ER  -

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Author Information

Chenjun Zhang

Department of Cardiology Gong Li Hospital, Affiliated to the Second Military Medical University, Shanghai, China
Jiahong Xu

Department of Cardiology Gong Li Hospital, Affiliated to the Second Military Medical University, Shanghai, China

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Plain Text BibTeX RIS

APA Style

Chenjun Zhang, Jiahong Xu. (2022). A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature. Cardiology and Cardiovascular Research, 6(3), 81-85. https://doi.org/10.11648/j.ccr.20220603.11

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ACS Style

Chenjun Zhang; Jiahong Xu. A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature. Cardiol. Cardiovasc. Res. 2022, 6(3), 81-85. doi: 10.11648/j.ccr.20220603.11

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AMA Style

Chenjun Zhang, Jiahong Xu. A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature. Cardiol Cardiovasc Res. 2022;6(3):81-85. doi: 10.11648/j.ccr.20220603.11

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@article{10.11648/j.ccr.20220603.11,
  author = {Chenjun Zhang and Jiahong Xu},
  title = {A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature},
  journal = {Cardiology and Cardiovascular Research},
  volume = {6},
  number = {3},
  pages = {81-85},
  doi = {10.11648/j.ccr.20220603.11},
  url = {https://doi.org/10.11648/j.ccr.20220603.11},
  eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.ccr.20220603.11},
  abstract = {Left ventricular non-compaction cardiomyopathy (LVNC) has anatomic characters of prominent left ventricular trabeculation and deep recesses and relatively thiner compacted layer which can lead to structurally and functionally abnormal of heart muscle. Its pathogenesis predominantly be primary cardiomyopathy and also can be results of drug toxicity or response to acquired triggers. Our case is a 27 years old man who had appeared symptoms including dyspnea and palpitation caused by exertion about ten years and been found with atrial septal defect but had not performed intervention. Then he was admitted because of aggravation of symptoms and been diagnosed left ventricular non compaction after finished echocardiography. Afterwards because of symptomatic bradycardia he had pacemaker implantation, but three months later he died of decompensated acute heart failure. LVNC has variable clinical manifestations including heart failure, thromboembolic events, ventricular arrhythmias and heart failure and the diagnosis of LVNC depends on echocardiography and Cardiac magnetic resonance mainly. Its mortality and morbidity are high and its classification as a specific cardiomyopathy be more appropriate. Therapy of end stage myocardial failure dependes on heart transplantation. Implanted cardioverter defibrillator (ICD) or cardiac resynchronization therapy defibrillator (CRTD) is the key method to prevent from sudden death. Risk stratification includes heart failure therapy, oral anticoagulation, heart transplantation and implantation of an automated defibrillator/cardioverter.},
 year = {2022}
}

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TY  - JOUR
T1  - A Poor Consequence Led by Left Ventricular Non-compaction: A Case Report and Review of Literature
AU  - Chenjun Zhang
AU  - Jiahong Xu
Y1  - 2022/10/11
PY  - 2022
N1  - https://doi.org/10.11648/j.ccr.20220603.11
DO  - 10.11648/j.ccr.20220603.11
T2  - Cardiology and Cardiovascular Research
JF  - Cardiology and Cardiovascular Research
JO  - Cardiology and Cardiovascular Research
SP  - 81
EP  - 85
PB  - Science Publishing Group
SN  - 2578-8914
UR  - https://doi.org/10.11648/j.ccr.20220603.11
AB  - Left ventricular non-compaction cardiomyopathy (LVNC) has anatomic characters of prominent left ventricular trabeculation and deep recesses and relatively thiner compacted layer which can lead to structurally and functionally abnormal of heart muscle. Its pathogenesis predominantly be primary cardiomyopathy and also can be results of drug toxicity or response to acquired triggers. Our case is a 27 years old man who had appeared symptoms including dyspnea and palpitation caused by exertion about ten years and been found with atrial septal defect but had not performed intervention. Then he was admitted because of aggravation of symptoms and been diagnosed left ventricular non compaction after finished echocardiography. Afterwards because of symptomatic bradycardia he had pacemaker implantation, but three months later he died of decompensated acute heart failure. LVNC has variable clinical manifestations including heart failure, thromboembolic events, ventricular arrhythmias and heart failure and the diagnosis of LVNC depends on echocardiography and Cardiac magnetic resonance mainly. Its mortality and morbidity are high and its classification as a specific cardiomyopathy be more appropriate. Therapy of end stage myocardial failure dependes on heart transplantation. Implanted cardioverter defibrillator (ICD) or cardiac resynchronization therapy defibrillator (CRTD) is the key method to prevent from sudden death. Risk stratification includes heart failure therapy, oral anticoagulation, heart transplantation and implantation of an automated defibrillator/cardioverter.
VL  - 6
IS  - 3
ER  -

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